Abstract

P 002

Foto essay: Axenfeld-Rieger syndrome with unilateral microcornea

Droutsas K., Kotoulas A., Papakonstantinou D., Georgopoulos G.
University of Athens, Department of Ophthalmology, Athens General Hospital "G.Gennimatas"

Objective: The purpose of this poster is to present a case of Axenfeld-Rieger syndrome with unilateral microcornea using photographs of the findings from the slit-lamp examination and gonioscopy.
Methods: A 23-year-old man was referred to us to investigate a lesion on the peripheral endothelium of his right cornea. The patient reported that his right eye had always been smaller than the left.
Results: Slit-lamp examination showed posterior embryotoxon, pigmented tissue on the posterior peripheral corneal surface and a slight traction of the pupil temporally. Gonioscopy revealed prominent Schwalbe line, multiple iris strands and mild iridodonesis. Visual acuity was 0.8 and intraocular pressure was 15 mmHg in both eyes. Corneal diameters were OD 10mm and OS 11mm. Axial lengths were OD 22,43mm and OS 23,55mm. Fundus examination, corneal topography, static perimetry and examination of patient’s parents and sister showed no pathological findings.
Conclusions: Axenfeld-Rieger syndrome is associated with several ocular and systemic anomalies. The combination of ARS with unilateral microcornea is rare. The recognition of ARS is important, as it reveals a glaucoma in 50% of cases.

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